Reticular erythematous mucinosis rem syndrome is a rare cutaneous disease first described by steigleder et al 1 more than 30 years ago. Reticular erythematous mucinosis is a chronic and rare syndrome of. Reticular erythematous mucinosis rem is a skin condition caused by fibroblasts producing abnormally large amounts of mucopolysaccharides. Reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin. This is a 28 year old woman who presents with a reticulated rash on her chest. Pdf sindrome rem associada a lupus eritematoso sistemico e. A repeat skin biopsy performed at our institute showed epidermal atrophy, hyalinization of collagen throughout the dermis and mucin deposition in upper reticular dermis figure 3a. Llinear morphea with secondary mucinosisinear morphea. What is reticular erythematous mucinosis reticular erythematous mucinosis rem is rare form of cutaneous mucinosis. These are the first cases of mucinosis described in mixed connective tissue disease.
Aug 01, 2012 reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Cutaneous mucinosis covers a heterogeneous group of diseases involving a diffuse and or focal mucin accumulation in the skin and its annexes. Includes pretibial myxedema of hyperthyroidism, generalized myxedema of hypothyroidism, papillary mucinosis lichen myxedematosus, myxoid cyst, cutaneous focal mucinosis, follicular mucinosis and carneys syndrome related myxoid nodules. Reticular erythematous mucinosis the icd10cm alphabetical index is designed to allow medical coders to look up various medical terms and connect them with the appropriate icd codes.
At present, almost 100 patients with rem syndrome have been described. Treatment of reticular erythematous mucinosis with uva1. Papulonodular mucinosis in systemic lupus erythematosus victoria g ortiz md a, ravi s krishnan md a, ling l chen md b, and sylvia hsu md a dermatology online journal 10 2. It is also called midline mucinosis or plaquelike cutaneous mucinosis. Mucinosis eritematosa reticular actas dermosifiliogr 2004. Reticular erythematous mucinosis rem syndrome is a rare, chronic disease characterized by asymptomatic, persistent reticular, slightly infiltrated erythematous plaques on chest andor back with slight infiltration. Reticular erythematous mucinosis and lupus erythematosus. Aug 01, 2011 includes pretibial myxedema of hyperthyroidism, generalized myxedema of hypothyroidism, papillary mucinosis lichen myxedematosus, myxoid cyst, cutaneous focal mucinosis, follicular mucinosis and carneys syndrome related myxoid nodules. Learn more about reticular erythematous mucinosis from related diseases, pathways, genes and ptms with the novus bioinformatics tool. Papulonodular mucinosis in systemic lupus erythematosus. Papules small bumps develop on the midback or chest and form a netlike pattern hence the name, reticular. These findings point to the diagnosis of reticular mucinosis. Although the exact etiology remains undefined, efforts to elucidate pathogenesis, disease associations, and prospective. Induction of the disease has been associated with viral processes, solar irradiation, specific.
Reticular erythematous mucinosis primary care dermatology. Reticular erythematous mucinosis rem is a rare chronic dermatosis that is typically characterized by reticular macular erythema or erythematous papules and plaques on the central area of the chest and back of middleaged women. On alcian blue periodic acid schiff stain, abundant mucin deposition was demonstrated in the upper reticular dermis figure 3b. Jan 11, 2019 reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin. Although the exact etiology remains undefined, efforts to elucidate pathogenesis, disease associations, and prospective treatment modalities have been encouraging. Reticular erythematous mucinosis rem is a rare chronic dermatosis with a predilection for anterior and posterior trunk typically. Predominantly affecting middleaged women, rem syndrome skin lesions are typically located on the central area of the chest or on the upper back but may also spread to the upper abdomen. Suarezamor and others published mucinosis eritematosa reticular. Jan 06, 2010 reticular erythematous mucinosis rem is a rare chronic dermatosis with a predilection for anterior and posterior trunk typically. Cutaneous focal mucinosis is a skin condition characterized by a solitary nodule or papule 189. By continuing to use this site you consent to the use of cookies on your device as described in our cookie policy unless you have disabled them.
It is a disease that tends to affect women in the third and fourth decades of life. Background reticular erythematous mucinosis rem is an uncommon disease, the nosology and specific characteristics of which are controversial because most. Induction of the disease has been associated with viral processes, solar irradiation. The cutaneous mucinoses are a heterogeneous group of diseases in which mucin accumulates in the skin or within the hair follicle. Mucinosis eritematosa reticular actas dermosifiliograficas. Benign or noncancerous forms of follicular mucinosis benign, primary or. Reticular erythematous mucinosis rem, rem syndrome. Reticular erythematous mucinosis rem is a disorder of dermal mucin accumulation that has been reported throughout the world. Since it was not possible to relate these findings to any known syndrome, a combination of the main signs, reticular erythema and mucinosis, was used to name this entity rem syndrome. Courtesy of bryan anderson, md rarely, rem may occur on the extremities, head, neck, or groin, and there has been a single report of gingival involvement in a patient with typical lesions on the chest. Dermis sindrome rem o mucinosis reticular eritematosa. Although the exact etiology remains undefined, efforts to. Appm is a mucinosis subtype which has a benign and. Reticular erythematous mucinosis is a rare syndrome which can be misdiagnosed as seborrhoeic dermatitis.
Benign or noncancerous forms of follicular mucinosis benign, primary or idiopathic follicular mucinosis are often of unknown cause. Sometimes follicular mucinosis may show up in skin biopsy results for other inflammatory skin diseases. Multiple lesions may indicate the carney complex in which the benign tumours may develop in the. Reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Jul 12, 2012 reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Mucinous disorders of the skinbeyond the dermal mucinosis. Is there a home remedy for reticular erythematous mucinosis. Reticular erythematous mucinosis the doctors doctor. Examination of biopsy specimen showed focal mucin deposition in papillary and upper reticular dermis. Icd10cm alphabetical index reticular erythematous mucinosis. Cutaneous mucinosis in mixed connective tissue disease ncbi.
Reticular erythematous mucinosis rem is a rare entity characterized by infiltrated erythematous plaques on exposed areas of the thorax and back. She has been on topical and oral steroids without resolution. It is caused by mucinous infiltration of tissues, and usually involves the scalp, face, and neck. Reticular erythematous mucinosis young to middle aged people women erythematous reticular or plaquelike eruption in the middle of the chest or back photoinduction. These are most commonly seen on the chest and upper back. Reticular erythematous mucinosis syndrome rem syndrome. Reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaquelike mucinosis and midline mucinosis. Cutaneous mucinosis in mixed connective tissue disease. Reticular erythematous mucinosis, journal of the european. The leading primary care society for dermatology and skin surgery. Follicular mucinosis definition of follicular mucinosis by.
There are 0 terms under the parent term reticular erythematous mucinosis in the icd10cm alphabetical index. Author links open overlay panel amalia serrano lourdes rodriguez julian s. Is there a home remedy for reticular erythematous mucinosis syndrome answered by a verified dermatologist we use cookies to give you the best possible experience on our website. Department of dermatology, national defense medical college, 32 namiki, tokorozawa, saitama 35985, japan.
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