At present, almost 100 patients with rem syndrome have been described. Follicular mucinosis definition of follicular mucinosis by. Although the exact etiology remains undefined, efforts to elucidate pathogenesis, disease associations, and prospective treatment modalities have been encouraging. Reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Examination of biopsy specimen showed focal mucin deposition in papillary and upper reticular dermis. Reticular erythematous mucinosis rem is a skin condition caused by fibroblasts producing abnormally large amounts of mucopolysaccharides.
Papules small bumps develop on the midback or chest and form a netlike pattern hence the name, reticular. Reticular erythematous mucinosis on the midline of the back article pdf available in cutis. Pdf sindrome rem associada a lupus eritematoso sistemico e. Focal cutaneous mucinosis see the pathology of focal cutaneous mucinosis. Reticular erythematous mucinosis the icd10cm alphabetical index is designed to allow medical coders to look up various medical terms and connect them with the appropriate icd codes. Appm is a mucinosis subtype which has a benign and. Reticular erythematous mucinosis young to middle aged people women erythematous reticular or plaquelike eruption in the middle of the chest or back photoinduction. Aug 01, 2012 reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. It is caused by mucinous infiltration of tissues, and usually involves the scalp, face, and neck.
Reticular erythematous mucinosis primary care dermatology. These findings point to the diagnosis of reticular mucinosis. Reticular erythematous mucinosis is a chronic and rare syndrome of. Icd10cm alphabetical index reticular erythematous mucinosis. Cutaneous focal mucinosis is a skin condition characterized by a solitary nodule or papule 189. Jan 11, 2019 reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin. The area is photosensitive and has been present for 1 year without resolution and without new lesions. Reticular erythematous mucinosis rem syndrome is a rare cutaneous disease first described by steigleder et al 1 more than 30 years ago. It presents with reticular, macular lesions or erythematous papules and plaques.
By continuing to use this site you consent to the use of cookies on your device as described in our cookie policy unless you have disabled them. Although the exact etiology remains undefined, efforts to. What is reticular erythematous mucinosis reticular erythematous mucinosis rem is rare form of cutaneous mucinosis. Papulonodular mucinosis in systemic lupus erythematosus victoria g ortiz md a, ravi s krishnan md a, ling l chen md b, and sylvia hsu md a dermatology online journal 10 2. Reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin. These are most commonly seen on the chest and upper back. Induction of the disease has been associated with viral processes, solar irradiation.
Reticular erythematous mucinosis rem is a rare entity characterized by infiltrated erythematous plaques on exposed areas of the thorax and back. Llinear morphea with secondary mucinosisinear morphea with. Learn more about reticular erythematous mucinosis from related diseases, pathways, genes and ptms with the novus bioinformatics tool. Reticular erythematous mucinosis, journal of the european. Although the exact etiology remains undefined, efforts to elucidate pathogenesis, disease associations, and prospective. It is also called midline mucinosis or plaquelike cutaneous mucinosis. Multiple lesions may indicate the carney complex in which the benign tumours may develop in the. It is a disease that tends to affect women in the third and fourth decades of life. Department of dermatology, national defense medical college, 32 namiki, tokorozawa, saitama 35985, japan. Cutaneous mucinosis in mixed connective tissue disease ncbi.
Dermis sindrome rem o mucinosis reticular eritematosa. Aug 01, 2011 includes pretibial myxedema of hyperthyroidism, generalized myxedema of hypothyroidism, papillary mucinosis lichen myxedematosus, myxoid cyst, cutaneous focal mucinosis, follicular mucinosis and carneys syndrome related myxoid nodules. Mucinosis eritematosa reticular actas dermosifiliogr 2004. The cutaneous mucinoses are a heterogeneous group of diseases in which mucin accumulates in the skin or within the hair follicle. Papulonodular mucinosis in systemic lupus erythematosus. Sometimes follicular mucinosis may show up in skin biopsy results for other inflammatory skin diseases. On alcian blue periodic acid schiff stain, abundant mucin deposition was demonstrated in the upper reticular dermis figure 3b. There are 0 terms under the parent term reticular erythematous mucinosis in the icd10cm alphabetical index. Reticular erythematous mucinosis rem is rare form of cutaneous mucinosis. Cutaneous mucinosis in mixed connective tissue disease.
Benign or noncancerous forms of follicular mucinosis benign, primary or idiopathic follicular mucinosis are often of unknown cause. Llinear morphea with secondary mucinosisinear morphea. This is a 28 year old woman who presents with a reticulated rash on her chest. Courtesy of bryan anderson, md rarely, rem may occur on the extremities, head, neck, or groin, and there has been a single report of gingival involvement in a patient with typical lesions on the chest. Jul 12, 2012 reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque.
Pdf reticular erythematous mucinosis on the midline of the back. Reticular erythematous mucinosis definition of reticular. Reticular erythematous mucinosis rem, rem syndrome. She has been on topical and oral steroids without resolution. These are the first cases of mucinosis described in mixed connective tissue disease. Benign or noncancerous forms of follicular mucinosis benign, primary or. Includes pretibial myxedema of hyperthyroidism, generalized myxedema of hypothyroidism, papillary mucinosis lichen myxedematosus, myxoid cyst, cutaneous focal mucinosis, follicular mucinosis and carneys syndrome related myxoid nodules. Reticular erythematous mucinosis is a rare syndrome which can be misdiagnosed as seborrhoeic dermatitis. The leading primary care society for dermatology and skin surgery. Suarezamor and others published mucinosis eritematosa reticular. Background reticular erythematous mucinosis rem is an uncommon disease, the nosology and specific characteristics of which are controversial because most reports deal with single cases or small series. A repeat skin biopsy performed at our institute showed epidermal atrophy, hyalinization of collagen throughout the dermis and mucin deposition in upper reticular dermis figure 3a. Cutaneous mucinosis covers a heterogeneous group of diseases involving a diffuse and or focal mucin accumulation in the skin and its annexes.
Reticular erythematous mucinosis rem is a disorder of dermal mucin accumulation that has been reported throughout the world. Clinical features and efficacy of antimalarial treatment for. Treatment of reticular erythematous mucinosis with uva1. Reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaquelike mucinosis and midline mucinosis. Reticular erythematous mucinosis rem is a rare chronic dermatosis with a predilection for anterior and posterior trunk typically. Background reticular erythematous mucinosis rem is an uncommon disease, the nosology and specific characteristics of which are controversial because most. Reticular erythematous mucinosis syndrome rem syndrome. Reticular erythematous mucinosis the doctors doctor. Author links open overlay panel amalia serrano lourdes rodriguez julian s. Dermis mucinose eritematosa reticulada information on the. Is there a home remedy for reticular erythematous mucinosis syndrome answered by a verified dermatologist we use cookies to give you the best possible experience on our website. Reticular erythematous mucinosis and lupus erythematosus. Reticular erythematous mucinosis rem syndrome is a rare, chronic disease characterized by asymptomatic, persistent reticular, slightly infiltrated erythematous plaques on chest andor back with slight infiltration. Since it was not possible to relate these findings to any known syndrome, a combination of the main signs, reticular erythema and mucinosis, was used to name this entity rem syndrome.
Induction of the disease has been associated with viral processes, solar irradiation, specific. Mucinosis eritematosa reticular reticular erythematous mucinosis. Predominantly affecting middleaged women, rem syndrome skin lesions are typically located on the central area of the chest or on the upper back but may also spread to the upper abdomen. Mucinosis eritematosa reticular actas dermosifiliograficas. Jan 06, 2010 reticular erythematous mucinosis rem is a rare chronic dermatosis with a predilection for anterior and posterior trunk typically. Reticular erythematous mucinosis rem is a rare chronic dermatosis that is typically characterized by reticular macular erythema or erythematous papules and plaques on the central area of the chest and back of middleaged women. Mucinous disorders of the skinbeyond the dermal mucinosis. Mar 26, 2010 is there a home remedy for reticular erythematous mucinosis syndrome answered by a verified dermatologist we use cookies to give you the best possible experience on our website. Is there a home remedy for reticular erythematous mucinosis.
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